Pathophysiology

Pathophysiology

I-3. Heart failure: causes and symptoms

心不全の原因と症状

What is Heart Failure?

  • A clinical syndrome of progressive weakening of the heart’s pump function, causing changes at systemic, organ, and cellular levels.
  • Ultimately leads to death via progressive loss of myocardial cells and arrhythmias.
  • Prevalence is rising with the aging population.

Classification

  • Acute vs chronic — by speed of onset (acute, e.g. myocardial infarction).
  • Forward vs backward:
    • Forward failure — cannot pump forward → ↓systemic perfusion (cyanosis).
    • Backward failure — cannot clear venous blood → congestion in lungs and/or systemic veins.
  • Systolic vs diastolic (Ejection fraction, EF = SV/EDV; healthy 55–75%):
    • Diastolic dysfunction — EF 35–50% (HFpEF, preserved EF).
    • Systolic dysfunction — EF <35% (HFrEF, reduced EF).
  • Left vs right sided.
  • Congestive HF — failure to clear blood from behind → congestion.

Symptoms by location

  • Left-sided, backward → LA + pulmonary congestion → pulmonary edema: rales, dyspnea, orthopnea, paroxysmal nocturnal dyspnea.
  • Left-sided, forward → weakness/fatigue (↓O₂ supply), nycturia (at rest at night, blood redistributes to kidneys → ↑urine).
  • Right-sided, backward (from ↑pulmonary pressure) → edema, hydrothorax, congestive hepatomegaly (nutmeg liver), distended neck veins, cyanosis, S3 gallop.

Provoking & Exacerbating Factors

  • Underlying (true) causes: ischemic heart disease, hypertension (↑afterload → ↑O₂ demand), diabetes (coronary vascular damage), cardiomyopathies, valvular heart disease.
  • Precipitating/decompensating factors (don’t cause HF but worsen it):
    • Increased workload: volume overload (renal failure, high Na⁺), pressure overload (high BP, PE), ↑metabolic need (fever, infection, hyperthyroidism).
    • Same workload, weaker heart: ischemia (↓ATP), arrhythmia, endo-/myocarditis, drug effects.

Diagnosis

  1. History + symptoms + physical exam.
  2. ECG (non-specific; a fully normal ECG can exclude HF) + chest X-ray.
  3. Biomarkers: BNP, NT-proBNP, ST2, hs-TnT — the worse the HF, the higher NT-proBNP.
  4. Echocardiography (measures EF).

Pressure–Volume Loop Changes

  • CO = HR × SV. Heart determinants: inotropy (contractility), lusitropy (relaxation/filling). Circulation: preload, afterload.
  • Isolated ↑HR doesn’t raise CO much — shorter diastole → less filling → weaker contraction (Frank-Starling).
  • PV-loop area = mechanical work (larger area = higher workload).
    • ↓Inotropy (systolic dysfunction): flatter end-systolic PV slope → smaller loop area = low workload.
    • ↓Lusitropy (diastolic dysfunction): less filling at the same end-diastolic pressure → smaller area = low workload.
  • Ischemia can cause both together: ↓O₂ → poor contraction (systolic) + stiffer muscle → poor filling (diastolic).

一問一答

What is heart failure?

A clinical syndrome of progressive weakening of the heart's pump function causing systemic, organ, and cellular changes, ultimately leading to death via myocardial cell loss and arrhythmias.

How is heart failure classified?

Acute vs chronic, forward vs backward, systolic vs diastolic, left vs right sided, and congestive (failure to clear blood → congestion).

What is the difference between forward and backward heart failure?

Forward failure: cannot pump blood forward → ↓systemic perfusion (cyanosis). Backward failure: cannot clear venous blood → congestion in lungs and/or systemic veins.

How are HFrEF and HFpEF defined by ejection fraction?

Healthy EF is 55–75%. Diastolic dysfunction = EF 35–50% (HFpEF, preserved); systolic dysfunction = EF <35% (HFrEF, reduced).

What are the symptoms of left-sided backward heart failure?

Left atrial + pulmonary congestion → pulmonary edema: rales, dyspnea, orthopnea, and paroxysmal nocturnal dyspnea.

What are the symptoms of left-sided forward heart failure?

Weakness/fatigue (↓O₂ supply) and nycturia (at rest at night, blood redistributes to the kidneys → ↑urine).

What are the main underlying (true) causes of heart failure?

Ischemic heart disease, hypertension (↑afterload → ↑O₂ demand), diabetes (coronary vascular damage), cardiomyopathies, and valvular heart disease.

What are the symptoms of right-sided backward heart failure?

Peripheral edema, hydrothorax, congestive hepatomegaly (nutmeg liver), distended neck veins, cyanosis, and an S3 gallop.

What is the difference between causes and precipitating factors of heart failure?

True causes produce HF (e.g., ischemia, hypertension), whereas precipitating/decompensating factors don't cause HF but worsen it (e.g., volume/pressure overload, fever, arrhythmia).

Which factors increase cardiac workload and can decompensate heart failure?

Volume overload (renal failure, high Na⁺), pressure overload (high BP, pulmonary embolism), and increased metabolic need (fever, infection, hyperthyroidism).

What biomarkers are used in diagnosing heart failure?

BNP, NT-proBNP, ST2, and hs-TnT; the worse the heart failure, the higher the NT-proBNP.

What is the gold-standard test for measuring ejection fraction in heart failure?

Echocardiography.

Why doesn't an isolated increase in heart rate raise cardiac output much?

Faster rate shortens diastole → less filling → weaker contraction (Frank-Starling), so CO does not rise proportionally.

What does the area of the pressure-volume loop represent, and how does it change in systolic dysfunction?

PV-loop area = mechanical work. In systolic dysfunction (↓inotropy), the end-systolic PV slope flattens → smaller loop area (lower work output).

How does the pressure-volume loop change in diastolic dysfunction?

↓Lusitropy means less filling at the same end-diastolic pressure → smaller loop area.

Why can ischemia cause both systolic and diastolic dysfunction?

↓O₂ impairs contraction (systolic) and makes the muscle stiffer, impairing filling (diastolic).

What determines cardiac output and its cardiac/circulatory components?

CO = HR × SV. Cardiac determinants: inotropy (contractility) and lusitropy (relaxation/filling). Circulatory determinants: preload and afterload.

What is the value of ECG in diagnosing heart failure?

It is non-specific, but a fully normal ECG can essentially exclude heart failure.

Why does congestive hepatomegaly occur in right heart failure, and what is its appearance?

Backward congestion of systemic veins backs blood up into the liver, producing a "nutmeg liver" appearance.

What commonly causes right-sided heart failure?

Increased pulmonary pressure (often from left-sided failure), which raises the right ventricle's workload.